Eosinophilic Esophagitis (EoE)

Eosinophilic Esophagitis (EoE)

TL;DR Eosinophilic esophagitis (EoE) is a chronic, immune/antigen-mediated esophageal disease. It’s characterized by eosinophil-predominant inflammation. Epidemiology ▾: Increasing prevalence, particularly in children and young adults. Male predominance. Linked...
AL Amyloidosis (Primary Amyloidosis)

AL Amyloidosis (Primary Amyloidosis)

TL;DR AL amyloidosis is a systemic disease caused by a clonal plasma cell disorder, leading to the production and deposition of abnormal light-chain amyloid fibrils in organs and tissues. Pathophysiology ▾: Abnormal plasma cells overproduce light chains that misfold,...
Sjögren’s Syndrome

Sjögren’s Syndrome

TL;DR Sjögren’s syndrome is a systemic autoimmune disease primarily targeting exocrine glands (dry eyes, mouth). Pathophysiology ▾: Lymphocytic infiltration, autoantibody production (anti-Ro/SSA, anti-La/SSB), genetic predisposition, and potential environmental...
Waldenström Macroglobulinemia

Waldenström Macroglobulinemia

TL;DR Waldenström macroglobulinemia (WM) is a rare, slow-growing B-cell lymphoma characterized by the overproduction of IgM monoclonal immunoglobulin by lymphoplasmacytic lymphoma (LPL) cells. Pathophysiology ▾: Primarily driven by the MYD88 L265P mutation, leading to...